{
  "abstract": "Erdheim-Chester disease (ECD) is a rare histiocytosis driven by somatic mutations involving genes of the MAPK pathway (e.g., BRAFV600E).1 Bilateral perirenal and retroperitoneal involvement occurs in approximately 70% of cases and typically consists of infiltration of the perirenal space (“hairy kidney” appearance), the pelvis, the proximal ureter, and the renal vascular peduncle2 (Figure 1a–f). It is often asymptomatic but may cause abdominal or lumbar pain and renovascular hypertension. Unrecognized long-standing perirenal infiltration can lead to obstructive or ischemic nephropathy, ultimately causing chronic kidney disease and, in some cases, kidney failure.",
  "abstract_shown": true,
  "affiliations": [],
  "article_type": null,
  "arxiv": null,
  "author_total": 15,
  "authors": [
    {
      "name": "Giulia Palazzini"
    },
    {
      "name": "Francesco Pegoraro"
    },
    {
      "name": "Jean-François Emile"
    },
    {
      "name": "Sanjeev Akkina"
    },
    {
      "name": "Elisa Buti"
    },
    {
      "name": "Anna Perrone"
    },
    {
      "name": "Corrado Campochiaro"
    },
    {
      "name": "Lorenzo Dagna"
    },
    {
      "name": "Edoardo La Porta"
    },
    {
      "name": "Decimo Silvio Chiarenza"
    },
    {
      "name": "Anna J. Peired"
    },
    {
      "name": "Achille Aouba"
    },
    {
      "name": "Raphaële Renard-Penna"
    },
    {
      "name": "Julien Haroche"
    },
    {
      "name": "Augusto Vaglio"
    }
  ],
  "bibtex": "https://research.draconitic.com/paper/d94pg4ap8nxdk.bib",
  "cited_by": 0,
  "doi": "10.1016/j.ekir.2025.103763",
  "fulltext_url": null,
  "id": "d94pg4ap8nxdk",
  "issns": [
    "2468-0249"
  ],
  "landing_url": "https://hal.science/hal-05849907v1",
  "language": "en",
  "licence": "CC-BY",
  "licence_label": "CC BY",
  "licence_source": "journal",
  "licence_url": "https://creativecommons.org/licenses/by/4.0/",
  "metadata_licence": null,
  "native_subjects": [
    [
      "hal",
      "0.sdv"
    ],
    [
      "openalex",
      "2747|Renal Transplantation Outcomes and Treatments"
    ]
  ],
  "openalex": "W7118036825",
  "pdf_url": "https://www.kireports.org/article/S2468-0249(25)00781-8/pdf",
  "pmcid": null,
  "pmid": "41660593",
  "published": "2026-11-03",
  "publisher": "Elsevier",
  "ris": "https://research.draconitic.com/paper/d94pg4ap8nxdk.ris",
  "sources": [
    {
      "first_seen": "2026-11-03T12:20:19Z",
      "native_id": "hal-05849907",
      "source": "hal",
      "url": "https://hal.science/hal-05849907v1"
    }
  ],
  "subjects": [
    {
      "field": "medicine",
      "origin": "openalex:2747|Renal Transplantation Outcomes and Treatments",
      "subfield": "surgery"
    }
  ],
  "title": "Kidney Transplantation in Patients With Erdheim-Chester Disease",
  "title_text": "Kidney Transplantation in Patients With Erdheim-Chester Disease",
  "type": "peer-reviewed",
  "updated_at": "2026-11-05T12:20:12Z",
  "url": "https://research.draconitic.com/paper/d94pg4ap8nxdk",
  "venue": "Kidney International Reports",
  "versions": []
}