Hilar cholangiocarcinoma associated with pancreaticobiliary maljunction, pancreas divisum, and a type V right hepatic duct variant: a case report
- 1Department of Hepatobiliary Surgery, Qingdao Municipal Hospital , ,
Abstract
This case describes hilar cholangiocarcinoma with pancreaticobiliary maljunction (PBM), pancreas divisum, and a type V right hepatic duct variant. Preoperative computed tomography (CT) with three-dimensional (3D) reconstruction and magnetic resonance cholangiopancreatography (MRCP) clarified the complex ductal anatomy and informed reconstruction. After local extrahepatic bile duct resection with hilar lymphadenectomy, the patient initially recovered uneventfully. At 5 months, CA19-9 was 4,360 U/mL, CEA was within the reference range, and imaging raised concern for recurrence. The patient died at home 6 months after surgery; multiorgan failure was reported, but no autopsy was performed. This case emphasises the need for detailed preoperative mapping of coexisting biliary and pancreatic ductal variants to guide operative planning and biliary reconstruction. It also illustrates the potential oncological limitations of local extrahepatic bile duct resection in the setting of incomplete disease staging.
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BibTeX
@article{dong2026hilar,
title = {{Hilar cholangiocarcinoma associated with pancreaticobiliary maljunction, pancreas divisum, and a type V right hepatic duct variant: a case report}},
author = {Ruipeng Dong and Peipei Cong and Guangjun Shi},
journal = {Frontiers in surgery},
year = {2026},
month = oct,
doi = {10.3389/fsurg.2026.1931578},
url = {https://europepmc.org/article/PMC/PMC13724584},
note = {CC BY},
}
RIS
TY - JOUR
TI - Hilar cholangiocarcinoma associated with pancreaticobiliary maljunction, pancreas divisum, and a type V right hepatic duct variant: a case report
AU - Ruipeng Dong
AU - Peipei Cong
AU - Guangjun Shi
PY - 2026
DA - 2026/10/19
JO - Frontiers in surgery
DO - 10.3389/fsurg.2026.1931578
UR - https://europepmc.org/article/PMC/PMC13724584
AB - This case describes hilar cholangiocarcinoma with pancreaticobiliary maljunction (PBM), pancreas divisum, and a type V right hepatic duct variant. Preoperative computed tomography (CT) with three-dimensional (3D) reconstruction and magnetic resonance cholangiopancreatography (MRCP) clarified the complex ductal anatomy and informed reconstruction. After local extrahepatic bile duct resection with hilar lymphadenectomy, the patient initially recovered uneventfully. At 5 months, CA19-9 was 4,360 U/mL, CEA was within the reference range, and imaging raised concern for recurrence. The patient died at home 6 months after surgery; multiorgan failure was reported, but no autopsy was performed. This case emphasises the need for detailed preoperative mapping of coexisting biliary and pancreatic ductal variants to guide operative planning and biliary reconstruction. It also illustrates the potential oncological limitations of local extrahepatic bile duct resection in the setting of incomplete disease staging.
SN - 2296-875X
ER -