Syringocystadenoma Papilliferum in an Adolescent with Grade 3 Microtia and Facial Nerve Palsy: A Rare Case Report with Literature Review
- 1Department of Otorhinolaryngology, Dr. D. Y. Patil Medical College, Hospital and Research Centre, Pune, Maharashtra, India
Abstract
Syringocystadenoma Papilliferum (SCAP) is rare clinical entities with atypical presentation that lead to diagnostic challenges. We describe a case of a 13-year-old male who had foul-smelling right postauricular discharge for 4-month and progressive worsening of childhood-onset hearing loss. Examination revealed House–Brackmann grade I facial palsy on the right side and grade 3 microtia with mild conductive hearing loss. High-resolution computed tomography and magnetic resonance imaging of the temporal bone showed sclerosis of the right mastoid air cells along with inflammatory changes. Right tympanomastoid exploration revealed a mass in the right postauricular region, and histopathology confirmed the diagnosis. An abnormal course of the right facial nerve was present. The facial nerve was transected intraoperatively followed by reconstruction with a greater auricular nerve graft, which led to House–Brackmann grade V facial nerve palsy and improved gradually with physical therapy. Thus, SCAP should be a differential diagnosis in pediatric patients who present with postauricular discharge, microtia, and facial nerve palsy, to ensure timely surgery and favorable outcomes.
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BibTeX
@article{verma2026syringocystadenoma,
title = {{Syringocystadenoma Papilliferum in an Adolescent with Grade 3 Microtia and Facial Nerve Palsy: A Rare Case Report with Literature Review}},
author = {Aishwarya Verma and Pooja Shriwastav and Paresh Chavan and Manu S. Babu and Mayur Ingale},
journal = {Annals of African Medicine},
year = {2026},
month = jul,
doi = {10.4103/aam.aam_58_26},
url = {https://doi.org/10.4103/aam.aam_58_26},
note = {CC BY-NC-SA 4.0},
}
RIS
TY - JOUR
TI - Syringocystadenoma Papilliferum in an Adolescent with Grade 3 Microtia and Facial Nerve Palsy: A Rare Case Report with Literature Review
AU - Aishwarya Verma
AU - Pooja Shriwastav
AU - Paresh Chavan
AU - Manu S. Babu
AU - Mayur Ingale
PY - 2026
DA - 2026/07/15
JO - Annals of African Medicine
DO - 10.4103/aam.aam_58_26
UR - https://doi.org/10.4103/aam.aam_58_26
AB - Syringocystadenoma Papilliferum (SCAP) is rare clinical entities with atypical presentation that lead to diagnostic challenges. We describe a case of a 13-year-old male who had foul-smelling right postauricular discharge for 4-month and progressive worsening of childhood-onset hearing loss. Examination revealed House–Brackmann grade I facial palsy on the right side and grade 3 microtia with mild conductive hearing loss. High-resolution computed tomography and magnetic resonance imaging of the temporal bone showed sclerosis of the right mastoid air cells along with inflammatory changes. Right tympanomastoid exploration revealed a mass in the right postauricular region, and histopathology confirmed the diagnosis. An abnormal course of the right facial nerve was present. The facial nerve was transected intraoperatively followed by reconstruction with a greater auricular nerve graft, which led to House–Brackmann grade V facial nerve palsy and improved gradually with physical therapy. Thus, SCAP should be a differential diagnosis in pediatric patients who present with postauricular discharge, microtia, and facial nerve palsy, to ensure timely surgery and favorable outcomes.
SN - 1596-3519
SN - 0975-5764
ER -