Joint Expert Consensus Report on the Diagnosis and Management of Pulmonary Arterial Hypertension in Türkiye In collaboration with Turkish Society of Cardiology, Turkish Thoracic Society and Pulmonary Vascular Disease Research Association (ADHAD)
11 affiliations
- 1Department of Cardiology, Cerrahpaşa Faculty of Medicine, İstanbul University-Cerrahpaşa, İstanbul, Türkiye
- 2Department of Cardiology, Faculty of Medicine, Firat University, Elazığ, Türkiye
- 3Department of Internal Medicine, Division of Rheumatology, Faculty of Medicine, Hacettepe University, Ankara, Türkiye
- 4Department of Cardiology, Pendik Training and Research Hospital, Marmara University, İstanbul, Türkiye
- 5Department of Internal Medicine, Division of Rheumatology, Cerrahpaşa Faculty of Medicine, İstanbul University-Cerrahpaşa, İstanbul, Türkiye
- 6Department of Cardiology, Faculty of Medicine, Hacettepe University, Ankara, Türkiye
- 7Department of Cardiology, Cardiology Institute, İstanbul University-Cerrahpaşa, İstanbul, Türkiye
- 8Department of Pulmonology, Faculty of Medicine, İstanbul University, İstanbul, Türkiye
- 9Department of Pulmonology, Faculty of Medicine, Ankara University, Ankara, Türkiye
- 10Department of Cardiology, Faculty of Medicine, Dokuz Eylül University, İzmir, Türkiye
- 11Department of Pulmonary Medicine, İstanbul Faculty of Medicine, İstanbul University, İstanbul, Türkiye
Abstract
Pulmonary arterial hypertension (PAH) is a progressive and life-threatening disease characterized by increased pulmonary vascular resistance and right ventricular (RV) dysfunction, requiring early diagnosis and timely management. This joint expert consensus report, developed in collaboration with the Turkish Society of Cardiology, Turkish Thoracic Society, and Pulmonary Vascular Disease Research Association (ADHAD), provides a practical, real-world framework for the diagnosis and management of PAH in Türkiye. The document presents updated, practice-oriented diagnostic algorithms designed to facilitate early recognition and accurate classification of PAH. A key objective is the standardization of data collection across centers; therefore, recommended echocardiographic and hemodynamic parameters, along with their normal and pathological ranges, are clearly defined to improve consistency in clinical evaluation and reporting. Risk assessment remains a cornerstone of patient evaluation; however, current guideline-based models have important limitations. In a disease with high mortality such as PAH, greater emphasis should be placed on dynamic risk evaluation at follow-up, incorporating detailed RV assessment through imaging and hemodynamic parameters, and enabling more timely treatment escalation when needed. Accordingly, treatment algorithms have been updated to reflect contemporary therapeutic strategies, emphasizing early combination therapy, individualized management, and prompt escalation in patients who fail to achieve or maintain a low-risk profile with particular attention to RV performance. Overall, this consensus aims to harmonize clinical practice, enhance data quality, and support more proactive and standardized management of PAH across Türkiye.
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BibTeX
@article{avcı2026joint,
title = {{Joint Expert Consensus Report on the Diagnosis and Management of Pulmonary Arterial Hypertension in Türkiye In collaboration with Turkish Society of Cardiology, Turkish Thoracic Society and Pulmonary Vascular Disease Research Association (ADHAD)}},
author = {Burçak Kılıçkıran Avcı and Mehmet Akbulut and Ali Akdoğan and Halil Ataş and Gülen Hatemi and Ergün Barış Kaya and M. Serdar Küçükoğlu and Bülent Mutlu and Gülfer Okumuş and Zeynep Pınar Önen and Bahri Akdeniz and Zeki Öngen and Züleyha Bingöl},
journal = {Anatolian Journal of Cardiology},
year = {2026},
month = oct,
doi = {10.14744/anatoljcardiol.2026.6648},
url = {https://doi.org/10.14744/anatoljcardiol.2026.6648},
note = {CC BY-NC 4.0},
}
RIS
TY - JOUR
TI - Joint Expert Consensus Report on the Diagnosis and Management of Pulmonary Arterial Hypertension in Türkiye In collaboration with Turkish Society of Cardiology, Turkish Thoracic Society and Pulmonary Vascular Disease Research Association (ADHAD)
AU - Burçak Kılıçkıran Avcı
AU - Mehmet Akbulut
AU - Ali Akdoğan
AU - Halil Ataş
AU - Gülen Hatemi
AU - Ergün Barış Kaya
AU - M. Serdar Küçükoğlu
AU - Bülent Mutlu
AU - Gülfer Okumuş
AU - Zeynep Pınar Önen
AU - Bahri Akdeniz
AU - Zeki Öngen
AU - Züleyha Bingöl
PY - 2026
DA - 2026/10/19
JO - Anatolian Journal of Cardiology
DO - 10.14744/anatoljcardiol.2026.6648
UR - https://doi.org/10.14744/anatoljcardiol.2026.6648
AB - Pulmonary arterial hypertension (PAH) is a progressive and life-threatening disease characterized by increased pulmonary vascular resistance and right ventricular (RV) dysfunction, requiring early diagnosis and timely management. This joint expert consensus report, developed in collaboration with the Turkish Society of Cardiology, Turkish Thoracic Society, and Pulmonary Vascular Disease Research Association (ADHAD), provides a practical, real-world framework for the diagnosis and management of PAH in Türkiye. The document presents updated, practice-oriented diagnostic algorithms designed to facilitate early recognition and accurate classification of PAH. A key objective is the standardization of data collection across centers; therefore, recommended echocardiographic and hemodynamic parameters, along with their normal and pathological ranges, are clearly defined to improve consistency in clinical evaluation and reporting. Risk assessment remains a cornerstone of patient evaluation; however, current guideline-based models have important limitations. In a disease with high mortality such as PAH, greater emphasis should be placed on dynamic risk evaluation at follow-up, incorporating detailed RV assessment through imaging and hemodynamic parameters, and enabling more timely treatment escalation when needed. Accordingly, treatment algorithms have been updated to reflect contemporary therapeutic strategies, emphasizing early combination therapy, individualized management, and prompt escalation in patients who fail to achieve or maintain a low-risk profile with particular attention to RV performance. Overall, this consensus aims to harmonize clinical practice, enhance data quality, and support more proactive and standardized management of PAH across Türkiye.
SN - 2149-2263
SN - 2149-2271
ER -