Peer-reviewedCC BY-NC-NDRespirology case reports
Cystic Lung Changes in Inclusion Body Myositis: An Unusual Pulmonary Manifestation.
- 1Northwest Lung Centre Wythenshawe Hospital, Manchester University NHS Foundation Trust Manchester UK.
- 2Department of Rheumatology, Salford Royal Hospital, Northern Care Alliance NHS Foundation Trust Manchester Academic Health Science Centre Salford UK.
- 3Division of Musculoskeletal and Dermatological Sciences, Faculty of Biology, Medicine and Health The University of Manchester Manchester UK.
Abstract
Idiopathic inflammatory myopathies (IIMs) are chronic autoimmune disorders affecting skeletal muscles, with pulmonary involvement in 30%-40% of cases. Inclusion body myositis (IBM) is a distinct subset that usually does not involve the lungs. This report highlights a rare case of inclusion body myositis presenting with pulmonary disease.
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BibTeX
@article{othman2026cystic,
title = {{Cystic Lung Changes in Inclusion Body Myositis: An Unusual Pulmonary Manifestation.}},
author = {Gehad Othman and Thasniya Ummer and Heshani De Silva and Harshana Bandara and Hector Chinoy},
journal = {Respirology case reports},
year = {2026},
month = oct,
doi = {10.1002/rcr2.70721},
url = {https://europepmc.org/article/MED/42903715},
note = {CC BY-NC-ND},
}
RIS
TY - JOUR
TI - Cystic Lung Changes in Inclusion Body Myositis: An Unusual Pulmonary Manifestation.
AU - Gehad Othman
AU - Thasniya Ummer
AU - Heshani De Silva
AU - Harshana Bandara
AU - Hector Chinoy
PY - 2026
DA - 2026/10/20
JO - Respirology case reports
DO - 10.1002/rcr2.70721
UR - https://europepmc.org/article/MED/42903715
AB - Idiopathic inflammatory myopathies (IIMs) are chronic autoimmune disorders affecting skeletal muscles, with pulmonary involvement in 30%-40% of cases. Inclusion body myositis (IBM) is a distinct subset that usually does not involve the lungs. This report highlights a rare case of inclusion body myositis presenting with pulmonary disease.
SN - 2051-3380
ER -