Isolated systemic arterial supply to the normal lung presenting with massive hemoptysis in a child: CT angiographic diagnosis and endovascular management
- 1Department of Radiodiagnosis and Interventional Radiology, VMMC and Safdarjung Hospital
Abstract
Isolated systemic supply to normal lung (ISSNL) is an uncommon bronchopulmonary vascular abnormality in which a section of normally ventilated lung gets arterial blood from the systemic circulation, without accompanying bronchial or pulmonary abnormalities. We discuss a case of a 12-year-old boy who had a single episode of significant hemoptysis. Computed tomographic angiography (CTA) identified a significant convoluted anomalous artery originating from the mid-descending thoracic aorta, supplying the left lower lobe, with no evidence of fistulous connection to pulmonary arteries. The diagnosis of ISSNL was confirmed, and the patient was effectively treated with endovascular embolization with a vascular plug. At the 3-month follow-up, no recurrence of hemoptysis was seen. While often asymptomatic, ISSNL may manifest as hemoptysis or signs of volume overload. CTA is essential for diagnosis, anatomical characterization, and treatment strategy formulation. Timely identification of this condition is crucial, since endovascular embolization provides a safe and effective alternative to surgical intervention with less morbidity.
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BibTeX
@article{singh2026isolated,
title = {{Isolated systemic arterial supply to the normal lung presenting with massive hemoptysis in a child: CT angiographic diagnosis and endovascular management}},
author = {Resham Singh and Vidushi Gupta and Renu Yadav and Rohini Gupta Ghasi},
journal = {Journal of Cardiothoracic Surgery},
year = {2026},
month = aug,
doi = {10.1186/s13019-026-04466-2},
url = {https://doi.org/10.1186/s13019-026-04466-2},
note = {CC BY},
}
RIS
TY - JOUR
TI - Isolated systemic arterial supply to the normal lung presenting with massive hemoptysis in a child: CT angiographic diagnosis and endovascular management
AU - Resham Singh
AU - Vidushi Gupta
AU - Renu Yadav
AU - Rohini Gupta Ghasi
PY - 2026
DA - 2026/08/01
JO - Journal of Cardiothoracic Surgery
DO - 10.1186/s13019-026-04466-2
UR - https://doi.org/10.1186/s13019-026-04466-2
AB - Isolated systemic supply to normal lung (ISSNL) is an uncommon bronchopulmonary vascular abnormality in which a section of normally ventilated lung gets arterial blood from the systemic circulation, without accompanying bronchial or pulmonary abnormalities. We discuss a case of a 12-year-old boy who had a single episode of significant hemoptysis. Computed tomographic angiography (CTA) identified a significant convoluted anomalous artery originating from the mid-descending thoracic aorta, supplying the left lower lobe, with no evidence of fistulous connection to pulmonary arteries. The diagnosis of ISSNL was confirmed, and the patient was effectively treated with endovascular embolization with a vascular plug. At the 3-month follow-up, no recurrence of hemoptysis was seen. While often asymptomatic, ISSNL may manifest as hemoptysis or signs of volume overload. CTA is essential for diagnosis, anatomical characterization, and treatment strategy formulation. Timely identification of this condition is crucial, since endovascular embolization provides a safe and effective alternative to surgical intervention with less morbidity.
SN - 1749-8090
ER -