The surgical outcome among children with congenital pseudoarthrosis of Tibia: Our 12 years of experience
- 1Department of Orthopedics, Hospital and Rehabilitation Center for Disabled Children (HRDC), Janagal, Banepa, Nepal
Abstract
Background: Congenital Pseudoarthrosis of the Tibia (CPT) is a rare condition characterized by poorly perfused, invasive hamartomatous fibrous tissue that leads to fracture and pseudoarthrosis of the tibia. Management challenges include achieving union and preventing refractures. This study aims to evaluate surgical interventions and their outcomes in managing congenital pseudoarthrosis of the tibia in children. Materials and methods: This retrospective study reviewed 70 CPT cases treated between 2010 and 2022 at Nepal’s only specialized center for children with physical disabilities. It assessed demographics, surgical procedures, and outcomes, with techniques including periosteal grafting and the Masquelet method. Union was defined radiologically, and analyses were conducted using MS Excel and SPSS. Results: This study included 70 CPT patients; 40 male (57.1%) and 30 female (42.9%). The mean age at presentation was 3.84 years, with the first surgery at 5.38 years. Most cases were Boyd type 5 (71.43%) and Crawford type 4 (71.43%). Of 35 patients who underwent surgery, the union rate was 41.93% (13/31), with a refracture rate of 23.08% among unions. Periosteal grafting had a 50% union rate, while the Masquelet technique achieved 41.67%. Conclusions: This study highlights the challenges in managing Congenital Pseudoarthrosis of the Tibia (CPT), emphasizing the need for personalized surgical approaches based on patient age, limb length discrepancy, and classification. Effective patient counseling on risks and benefits is crucial for informed decisions.
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BibTeX
@article{rajbhandari2026surgical,
title = {{The surgical outcome among children with congenital pseudoarthrosis of Tibia: Our 12 years of experience}},
author = {Tarun RajBhandari and Sabin Pokharel and Yam Prakash Gurung and Rajan Bhusal and Bibek Banskota and Ashok Kumar Banskota},
journal = {PLOS One},
year = {2026},
month = nov,
doi = {10.1371/journal.pone.0362359},
url = {https://doi.org/10.1371/journal.pone.0362359},
note = {CC BY 4.0},
}
RIS
TY - JOUR
TI - The surgical outcome among children with congenital pseudoarthrosis of Tibia: Our 12 years of experience
AU - Tarun RajBhandari
AU - Sabin Pokharel
AU - Yam Prakash Gurung
AU - Rajan Bhusal
AU - Bibek Banskota
AU - Ashok Kumar Banskota
PY - 2026
DA - 2026/11/05
JO - PLOS One
DO - 10.1371/journal.pone.0362359
UR - https://doi.org/10.1371/journal.pone.0362359
AB - Background: Congenital Pseudoarthrosis of the Tibia (CPT) is a rare condition characterized by poorly perfused, invasive hamartomatous fibrous tissue that leads to fracture and pseudoarthrosis of the tibia. Management challenges include achieving union and preventing refractures. This study aims to evaluate surgical interventions and their outcomes in managing congenital pseudoarthrosis of the tibia in children. Materials and methods: This retrospective study reviewed 70 CPT cases treated between 2010 and 2022 at Nepal’s only specialized center for children with physical disabilities. It assessed demographics, surgical procedures, and outcomes, with techniques including periosteal grafting and the Masquelet method. Union was defined radiologically, and analyses were conducted using MS Excel and SPSS. Results: This study included 70 CPT patients; 40 male (57.1%) and 30 female (42.9%). The mean age at presentation was 3.84 years, with the first surgery at 5.38 years. Most cases were Boyd type 5 (71.43%) and Crawford type 4 (71.43%). Of 35 patients who underwent surgery, the union rate was 41.93% (13/31), with a refracture rate of 23.08% among unions. Periosteal grafting had a 50% union rate, while the Masquelet technique achieved 41.67%. Conclusions: This study highlights the challenges in managing Congenital Pseudoarthrosis of the Tibia (CPT), emphasizing the need for personalized surgical approaches based on patient age, limb length discrepancy, and classification. Effective patient counseling on risks and benefits is crucial for informed decisions.
SN - 1932-6203
ER -