Quadricuspid Aortic Valve Presenting with Aortic Regurgitation in Adulthood: A Case Report
- 1Department of Cardiology, Dr. D. Y. Patil Medical College and Hospital, Pune, Maharashtra, India
Abstract
Quadricuspid aortic valve (QAV) is a rare congenital cardiac anomaly characterized by four aortic cusps instead of the normal three. It is most commonly associated with progressive aortic regurgitation and is often diagnosed incidentally on echocardiography. A woman in her fifties presented with palpitations and exertional dyspnea (New York Heart Association Class II). Clinical examination revealed an early diastolic murmur at the left sternal border. Transthoracic echocardiography demonstrated a QAV with Hurwitz and Roberts Type F morphology and moderate aortic regurgitation with preserved left ventricular systolic function. Transoesophageal echocardiography confirmed central cusp malcoaptation. The patient was managed conservatively and remained stable at 6-month follow-up. QAV is an uncommon congenital anomaly that may present in adulthood with aortic regurgitation. Echocardiography is essential for diagnosis and classification. Early recognition has important implications for surveillance and procedural planning.
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BibTeX
@article{nalawade2026quadricuspid,
title = {{Quadricuspid Aortic Valve Presenting with Aortic Regurgitation in Adulthood: A Case Report}},
author = {Digvijay Nalawade and Sanket Ashok Bari and Susheel Kumar Malani},
journal = {Annals of African Medicine},
year = {2026},
month = jun,
doi = {10.4103/aam.aam_154_26},
url = {https://doi.org/10.4103/aam.aam_154_26},
note = {CC BY-NC-SA 4.0},
}
RIS
TY - JOUR
TI - Quadricuspid Aortic Valve Presenting with Aortic Regurgitation in Adulthood: A Case Report
AU - Digvijay Nalawade
AU - Sanket Ashok Bari
AU - Susheel Kumar Malani
PY - 2026
DA - 2026/06/30
JO - Annals of African Medicine
DO - 10.4103/aam.aam_154_26
UR - https://doi.org/10.4103/aam.aam_154_26
AB - Quadricuspid aortic valve (QAV) is a rare congenital cardiac anomaly characterized by four aortic cusps instead of the normal three. It is most commonly associated with progressive aortic regurgitation and is often diagnosed incidentally on echocardiography. A woman in her fifties presented with palpitations and exertional dyspnea (New York Heart Association Class II). Clinical examination revealed an early diastolic murmur at the left sternal border. Transthoracic echocardiography demonstrated a QAV with Hurwitz and Roberts Type F morphology and moderate aortic regurgitation with preserved left ventricular systolic function. Transoesophageal echocardiography confirmed central cusp malcoaptation. The patient was managed conservatively and remained stable at 6-month follow-up. QAV is an uncommon congenital anomaly that may present in adulthood with aortic regurgitation. Echocardiography is essential for diagnosis and classification. Early recognition has important implications for surveillance and procedural planning.
SN - 1596-3519
SN - 0975-5764
ER -